Introduction: Status Electric Sleep (ESES) is characterized by a continued spike-wave activity during the slow sleep. This pattern is described associated with Landau Kleffner Syndrome (SLK), Epilepsy with Continuous Wave Sleep Spike Slow (EPOCSL) evolutions and atypical rolandic epilepsies (ER-EA). Cognitive impairment, behavioral and / or motor is part of the ESES.

Objective: Describe the clinical spectrum, etiology and management of 13 children with ESES

Methods: Review of clinical data and EEG / video-EEG of patients with ESES controlled  at the HCSBA Neuropsychiatry Service, from 2005 to 2013. We considered ESES if the continued spike-wave activity was seen in at least 85% of the slow sleep.

Results: 13 patients were analyzed. The mean age of seizure onset was 5 years and 6 months, the mean age of ESES onset was 6 years and 6 month. Related epileptic syndromes were ER-EA (8), EPOCSL (3) and likely SLK (2). With the onset of ESES 7 patients presented change of seizures pattern and all showed cognitive impairment and / or behavioral.  5 patients responded to treatment. Showed efficacy: the addition of benzodiazepines (2), clobazam, levetiracetam association (1), valproic (1) and prednisone(1). The duration of the ESES was variable (1 month-7 years).

Conclusion: ESES can be seen in various epileptic syndromes. We observed a change in the seizures pattern and behavioral cognitive impairment when ESES started. We observed response to most of treatments, however the deterioration was kept in most of the  cases. The persistence of the impairment is associated with duration of ESES.