Introduction: Paroxysmal Dyskinesias are involuntary intermittent movements, manifested with dystonia, chorea, athetosis , tribalism or a combination of them. They are secondary to ion channels defects.

Objectives: The aim of this study is to define the most frequent forms of presentation in our population and the management response.

Materials and Methods: Retrospective study of medical records of 15 patients with paroxysmal dyskinesias treated at our center between 1991-2010 .

Results: 15 patients, 6 women and 9 men were evaluated, all of them presented normal development and no oyher pathologies. 4 had family history of abnormal movements (3 were brothers, who also had febrile seizures history). The average age of onset was 3.9 years. Dystonia: 6 patients generalized, 3 patients hemidystonia (6 nonkinesigenic and 3 kinesigenic). Choreoathetosis: 5 generalized and 1 hemichorea, 4 of them were nonkinesigenic and 2 kinesigenic. All patienes had normal imaging, electrophysiological and metabolic studies. 7 patients received medical treatment with carbamazepine and 4 with acetazolamide, all of them with good clinical response.

Conclusion: In our study we found a male predomince in all dyskinesic patients. Dystonia were more common than choreoathetosis. Kinesigenic dyskinesia were predominan. There was a good response to symptomatic treatment . Three patients corresponded to a familial form of paroxysmal choreoathetosis with febrile seizures. We found no secondary causes.

Discussion: Although dyskinesias are often sporadic or familial and presented frequently spontaneous remission, it is important to look for secondary causes and discard epilepsy as the main differential diagnosis.