Last modified: 2018-09-09
Abstract
AIM:
Split cord malformation (SCM) is a rare congenital spinal abnormality. Antenatal features and Clinico-pathological features and surgical management strategies for Antenatal diagnosed Spilt Cord Malformation type 1[ASM] are discussed.
MATERIALS:
The Author reviewed records of 18 children who underwent surgical treatment for ASM August 2009 until May 2018. Their Antenatal Characteristic, Associated abnormality, clinical, radiological features and management including follow-up were analyzed. In 4 children were diagnosed before 20weeks gestational age, 6 cases between 20 to 28 weeks and 8 were after 28 weeks. In 5 cases a fetal MRI was performed. There were 10 males and 8 females, Age at surgery ranged from 5 months to 64 months with mean of 16.2 months.
RESULTS:
All the children underwent Detethering. Follow-up duration ranged from 1year to 6.3 years with mean of 33.2 months. All children good neurological outcome except 3 children, 2 children had neuroorthopedic deformity and one child had neurogenic bladder.
CONCLUSION:
In this Study Ultrasound remains the best tool to diagnose ASM. Postnatal and neurological outcome is favorable.